Main Article Content
Background: Caroli's disease (CD) is a rare congenital disorder. The early diagnosis of the disease and differentiation of types I and II are of extreme importance to patient survival. This case report was designed to review, discuss to clarify the clinical characteristics of the disease.
Methods: The demographic and clinical feature, laboratory indicators, imaging findings and pathology results were reviewed.
Results: Caroli's disease can occur at any age specially young age. Magnetic resonance cholangiopancreatography (MRCP) and computed tomography (CT) examinations were most useful in diagnosing CD.
Conclusions: No typical symptoms, signs or laboratory indicators are able to distinguish CD from other conditions. Both MRI and CT were most valuable in diagnosis.
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