Caroli’s Disease Presenting as Acute Cholangitis: A Case Report
M. Tahiri
Gastroenterology Unit, Ibn Rochd University Hospital of Casablanca, Hassan II University of Casablanca, Morocco.
S. EL Soussi *
Gastroenterology Unit, Ibn Rochd University Hospital of Casablanca, Hassan II University of Casablanca, Morocco.
D. Melieje
Gastroenterology Unit, Ibn Rochd University Hospital of Casablanca, Hassan II University of Casablanca, Morocco.
Z. Boukhal
Gastroenterology Unit, Ibn Rochd University Hospital of Casablanca, Hassan II University of Casablanca, Morocco.
FZ. EL Rhaoussi
Gastroenterology Unit, Ibn Rochd University Hospital of Casablanca, Hassan II University of Casablanca, Morocco.
F. Haddad
Gastroenterology Unit, Ibn Rochd University Hospital of Casablanca, Hassan II University of Casablanca, Morocco.
W. Hliwa
Gastroenterology Unit, Ibn Rochd University Hospital of Casablanca, Hassan II University of Casablanca, Morocco.
A. Bellabah
Gastroenterology Unit, Ibn Rochd University Hospital of Casablanca, Hassan II University of Casablanca, Morocco.
W. Badre
Gastroenterology Unit, Ibn Rochd University Hospital of Casablanca, Hassan II University of Casablanca, Morocco.
*Author to whom correspondence should be addressed.
Abstract
Caroli disease is a congenital disorder characterized by multifocal, segmental dilatation or ectasia of large intrahepatic bile ducts. The disease develops due to a remodeling defect, but its molecular pathogenesis is not fully understood. The absence of specific symptoms and signs in Caroli's disease complicates the diagnosis.
It is important to highlight this case and as many can be misdiagnosed by the gastro-enterologist and the surgeons.
Through the column of this article, we describe a 37 years old female to whom the clinical presentation, biological and the radiological findings were that of a Caroli’s disease misdiagnosed since 2012.
Keywords: Caroli’s disease, cholangitis, hydatid cyst